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Revista Costarricense de Cardiología

Print version ISSN 1409-4142

Abstract

PEREZ CARVAJAL, José Ignacio; FALLAS, Randall Quirós; VINDAS VILLAREAL, Manuel A.  and  VASQUEZ, Moisés. Estenosis Tricuspídea Severa secundaria a enfermedad carcinoide cardiaca: presentación de caso clínico y revisión de la literatura. Rev. costarric. cardiol [online]. 2023, vol.25, n.2, pp.37-44. ISSN 1409-4142.

Severe Tricuspid Stenosis Secondary to Cardiac Carcinoid Disease: Case Report and Literature Review

Tricuspid stenosis is an unfrequent valvulopathy that can be caused by multiple etiologies, including rheumatic disease and infectious endocarditis. In rare occasions, it occurs in the context of a carcinoid syndrome, in what is known as carcinoid heart disease. This condition causes fibrosis of the valves and the endocardium of the right ventricule, which can progress into right ventricular failure, worsening the patient's prognosis. In this article, we present a case of a severe tricuspid stenosis in which this ethiology is suspected. We show the echocardiographic images obtained for the diagnosis (two-dimensional imaging, multimodal imaging and 3D echocardiography), and we discuss the clinical and diagnostic implications, therapeutic options and prognosis of this rare condition.

Keywords : Tricuspid stenosis; carcinoid syndrome; right cardiac failure.

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