Abstract

LANZAS-RODRIGUEZ, Róger A  and  SALAS-SEGURA, Donato A. Miocardiopatía espongiforme o no campactada del ventrículo izquierdo. Acta méd. costarric [online]. 2006, vol.48, n.1, pp.35-38. ISSN 0001-6002.

Noncompaction of the ventricular myocardium or "spongy myocardium", is a rare congenital cardiomyopathy resulting from an arrest in normal endomyocardial embryogenesis. The characteristic echocardiographic findings of this disease consist of multiple myocardial trabeculations and deep intertrabecular recesses communicating with the left ventricular cavity. Familial occurrence has been observed linked to the Xq29 chromosome. Two cases in young black brothers are presented, both have the typical clinical and echocardiographic features of the disease, the diagnosis was made at the Tony Facio Castro Regional Hospital of Limón.

Keywords : spongy myocardium; non compaction of ventricular myocardium.