<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0001-6002</journal-id>
<journal-title><![CDATA[Acta Médica Costarricense]]></journal-title>
<abbrev-journal-title><![CDATA[Acta méd. costarric]]></abbrev-journal-title>
<issn>0001-6002</issn>
<publisher>
<publisher-name><![CDATA[Colegio de Médicos y Cirujanos de Costa Rica]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0001-60022016000300103</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Encefalitis por anticuerpos antirreceptor N-metil-D-aspartato]]></article-title>
<article-title xml:lang="en"><![CDATA[Anti N-methyl-D-aspartate receptor encephalitis]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Barquero-Madrigal]]></surname>
<given-names><![CDATA[Alejandro]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de Costa Rica Departamento de Bioquímica ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Costa Rica</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>09</month>
<year>2016</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>09</month>
<year>2016</year>
</pub-date>
<volume>58</volume>
<numero>3</numero>
<fpage>103</fpage>
<lpage>109</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_arttext&amp;pid=S0001-60022016000300103&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_abstract&amp;pid=S0001-60022016000300103&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_pdf&amp;pid=S0001-60022016000300103&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: La encefalitis por anticuerpos antirreceptor N-metil-D-Aspartato pertenece a un grupo de enfermedades que inicialmente se llamaban encefalitis límbicas, hoy conocidas como encefalitis autoinmunes. Se caracterizan por estar frecuentemente asociadas a algún tumor, responder a la inmunoterapia y provocar daños cerebrales variables que se manifiestan como cuadros clínicos polimorfos (desde la disfunción límbica hasta una encefalopatía multifocal o difusa). Algunos pacientes con condiciones psiquiátricas agudas podrían tener en realidad una encefalitis autoinmune, sin embargo, no es tan fácil sospecharlo con las manifestaciones iniciales. Su incidencia exacta no se conoce, pero cada vez hay más reportes de casos. Sus características clínicas están bien descritas y evolucionan en cinco fases. El diagnóstico definitivo se hace al obtener la confirmación serológica de los anticuerpos, pero hay algunas pruebas que pueden orientar la sospecha diagnóstica. El tratamiento se basa en esteroides y otros inmunosupresores.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: Anti NMDA-receptor encephalitis belongs to a group of diseases originally called limbic encephalitis, nowadays known as autoimmune encephalitis. These encephalitis are characterized by a frequent association with a tumor, a good response to immunotherapy, and by causing a broad range of brain injuries which manifest in polymorphous clinical pictures (from limbic dysfunction to multifocal or diffuse encephalopathy). Some patients diagnosed with acute psychiatry conditions may have instead autoimmune encephalitis. Nevertheless, it is not easy to discern one from the other in the initial stages. Its exact incidence is unknown, but there are increasingly more case reports. Its clinical characteristics are well described and evolve in five stages or phases. The final diagnosis is made when antibodies serologic confirmation is obtained, but some other tests may help guide the diagnosis. The treatment is based on steroids and other immunosuppressants.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[encefalitis autoinmune]]></kwd>
<kwd lng="es"><![CDATA[encefalitis por anticuerpos antiNMDA]]></kwd>
<kwd lng="es"><![CDATA[encefalitis paraneoplásica]]></kwd>
<kwd lng="es"><![CDATA[trastornos neuropsiquiátricos]]></kwd>
<kwd lng="en"><![CDATA[autoimmune encephalitis]]></kwd>
<kwd lng="en"><![CDATA[anti NMDA-receptor encephalitis]]></kwd>
<kwd lng="en"><![CDATA[paraneoplastic encephalitis]]></kwd>
<kwd lng="en"><![CDATA[neuropsychiatric disorders]]></kwd>
</kwd-group>
</article-meta>
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