<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2215-3411</journal-id>
<journal-title><![CDATA[Odovtos International Journal of Dental Sciences]]></journal-title>
<abbrev-journal-title><![CDATA[Odovtos]]></abbrev-journal-title>
<issn>2215-3411</issn>
<publisher>
<publisher-name><![CDATA[Facultad de Odontología. Universidad de Costa Rica]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2215-34112020000300054</article-id>
<article-id pub-id-type="doi">10.15517/ijds.2020.42072</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Dental Rehabilitation of a Rare Hallermann-Streiff Syndrome with Olygodontia: A Case Report]]></article-title>
<article-title xml:lang="es"><![CDATA[Rehabilitación dental de un caso raro de Síndrome de Hallermann- Streiff con Oligodoncia: Reporte de un caso]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Keskin]]></surname>
<given-names><![CDATA[Gül]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Tek]]></surname>
<given-names><![CDATA[Gün B.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Gaziantep University Faculty of Dentistry ]]></institution>
<addr-line><![CDATA[Gaziantep ]]></addr-line>
<country>Turkey</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Gaziantep University Faculty of Dentistry ]]></institution>
<addr-line><![CDATA[Gaziantep ]]></addr-line>
<country>Turkey</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<volume>22</volume>
<numero>3</numero>
<fpage>54</fpage>
<lpage>58</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_arttext&amp;pid=S2215-34112020000300054&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_abstract&amp;pid=S2215-34112020000300054&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_pdf&amp;pid=S2215-34112020000300054&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Hallermann-Streiff syndrome (HSS) is a rare oculomandibulofacial discephaly with hypotrichosis that occurs as a sporadic mutation. It is characterized by abnormal findings especially in head and face. Dental anomalies occur in 50-80% of the patients. In this case report, facial-oral findings and the existing dental anomalies of the syndrome in a 6-year-old male patient diagnosed with HSS were identified. Dental rehabilitation and a 12-month follow-up of the patient were reported. Each case presented with this rare syndrome may contribute to the literature to determine the prognosis of the disease and to take protective and preventive measures.]]></p></abstract>
<abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen El síndrome de Hallermann-Streiff (HSS) es una discefalia oculomandibulofacial rara con hipotricosis que ocurre como una mutación esporádica. Se caracteriza por hallazgos anormales, especialmente en cabeza y cara. Las anomalías dentales ocurren en 50-80% de los pacientes. En este reporte de caso, se identificaron los hallazgos faciales-orales y las anomalías dentales existentes del síndrome en un paciente masculino de 6 años diagnosticado con HSS. Se informó la rehabilitación dental y un seguimiento de 12 meses del paciente. Cada caso presentado con este síndrome raro puede contribuir a la literatura para determinar el pronóstico de la enfermedad y tomar medidas de protección y prevención.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Dental anomalies]]></kwd>
<kwd lng="en"><![CDATA[Hallermann-Streiff syndrome]]></kwd>
<kwd lng="en"><![CDATA[Tooth agenesis]]></kwd>
<kwd lng="en"><![CDATA[Primary dentition]]></kwd>
<kwd lng="en"><![CDATA[Nance appliance]]></kwd>
<kwd lng="en"><![CDATA[Pediatric dentistry]]></kwd>
<kwd lng="es"><![CDATA[Anomalías dentales]]></kwd>
<kwd lng="es"><![CDATA[Síndrome de Hallermann-Streiff]]></kwd>
<kwd lng="es"><![CDATA[Agenesia dental]]></kwd>
<kwd lng="es"><![CDATA[Dentición primaria]]></kwd>
<kwd lng="es"><![CDATA[Aparato nance]]></kwd>
<kwd lng="es"><![CDATA[Odontología pediátrica.]]></kwd>
</kwd-group>
</article-meta>
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