<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2215-3411</journal-id>
<journal-title><![CDATA[Odovtos International Journal of Dental Sciences]]></journal-title>
<abbrev-journal-title><![CDATA[Odovtos]]></abbrev-journal-title>
<issn>2215-3411</issn>
<publisher>
<publisher-name><![CDATA[Facultad de Odontología. Universidad de Costa Rica]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2215-34112020000200062</article-id>
<article-id pub-id-type="doi">10.15517/ijds.2020.40798</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Dental Findings in Kabuki Syndrome: A Systematic Review for Dentistry]]></article-title>
<article-title xml:lang="es"><![CDATA[Hallazgos dentales en el síndrome de Kabuki: Una revisión sistemática para la odontología]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Barbosa-Lima]]></surname>
<given-names><![CDATA[Ricardo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Lopes]]></surname>
<given-names><![CDATA[Amanda]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[N. F. de Moura]]></surname>
<given-names><![CDATA[Juliely]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ribeiro]]></surname>
<given-names><![CDATA[Sabrina N.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cardoso]]></surname>
<given-names><![CDATA[Matheus S. N. T.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Federal University of Sergipe Department of Dentistry of Lagarto ]]></institution>
<addr-line><![CDATA[Lagarto, Sergipe ]]></addr-line>
<country>Brazil</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Federal University of Sergipe Department of Medicine of Lagarto ]]></institution>
<addr-line><![CDATA[Lagarto, Sergipe ]]></addr-line>
<country>Brazil</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>08</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>08</month>
<year>2020</year>
</pub-date>
<volume>22</volume>
<numero>2</numero>
<fpage>62</fpage>
<lpage>71</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_arttext&amp;pid=S2215-34112020000200062&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_abstract&amp;pid=S2215-34112020000200062&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_pdf&amp;pid=S2215-34112020000200062&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: Kabuki syndrome consists in a series of congenital anomalies involving intellectual disability, hypotonia, and facial and body dysmorphism. In addition to these cardinal signs, craniofacial and dental changes are frequently observed, although they are not fully understood. Thus, the aim of this article is to present the dental findings in patients with Kabuki syndrome. This is a systematic review developed according to the PRISMA protocol. A search strategy with descriptors ("kabuki syndrome" AND "dentistry") was applied to six databases. As inclusion criteria, we selected clinical case reports that addressed dental findings in one or more patients with Kabuki syndrome between 1999 and 2019, without restrictions regarding gender, age or language. Data collection in all databases was performed by a calibrated evaluator and titles, abstracts and full-text studies were systematically analyzed. Eleven case reports that fit the proposed inclusion criteria were found. After the qualitative synthesis, teeth absence or agenesis were the most reported findings, being observed by nine authors. Less frequent dental findings in patients with this syndrome are taurodontism, microdontia, fusion, gemination and conical or screwdriver-shaped teeth. In fact, when any syndrome or genetic condition is related to manifestations of dental interest, the dental surgeon should be able to investigate them, especially teeth agenesis or absence. For this reason, the dentist should be aware of the manifestations of Kabuki syndrome, contributing to patients' understanding and management.]]></p></abstract>
<abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: El síndrome de Kabuki consiste en una serie de anomalías congénitas que involucran discapacidad intelectual, hipotonía y dismorfismo facial y corporal. Además de estos signos cardinales, con frecuencia se observan cambios craneofaciales y dentales, aunque no se entienden completamente. Por lo tanto, el objetivo de este artículo es presentar los hallazgos dentales en pacientes con síndrome de Kabuki. Esta es una revisión sistemática desarrollada de acuerdo con el protocolo PRISMA. Se aplicó una estrategia de búsqueda con descriptores ("síndrome de kabuki" AND "odontología") a seis bases de datos. Como criterios de inclusión, seleccionamos informes de casos clínicos que abordaban los hallazgos dentales en uno o más pacientes con síndrome de Kabuki entre 1999 y 2019, sin restricciones de género, edad o idioma. La recolección de datos en todas las bases de datos fue realizada por un evaluador calibrado y los títulos, resúmenes y estudios de texto completo fueron analizados sistemáticamente. Se encontraron once informes de casos que se ajustan a los criterios de inclusión propuestos. Después de la síntesis cualitativa, la ausencia de dientes o la agenesia fueron los hallazgos más reportados, siendo observados por nueve autores. Los hallazgos dentales menos frecuentes en pacientes con este síndrome son taurodoncia, microdoncia, fusión, geminación y dientes cónicos o con forma de destornillador. De hecho, cuando cualquier síndrome o condición genética se relaciona con manifestaciones de interés dental, el cirujano dental debe poder investigarlas, especialmente la agenesia o ausencia de los dientes. Por esta razón, el dentista debe ser consciente de las manifestaciones del síndrome de Kabuki, lo que contribuye a la comprensión y el manejo de los pacientes.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Kabuki syndrome]]></kwd>
<kwd lng="en"><![CDATA[Genetics]]></kwd>
<kwd lng="en"><![CDATA[Oral manifestations]]></kwd>
<kwd lng="en"><![CDATA[Tooth abnormalities]]></kwd>
<kwd lng="en"><![CDATA[Case reports]]></kwd>
<kwd lng="en"><![CDATA[Systematic review]]></kwd>
<kwd lng="es"><![CDATA[Síndrome de Kabuki]]></kwd>
<kwd lng="es"><![CDATA[Genética]]></kwd>
<kwd lng="es"><![CDATA[Manifestaciones orales]]></kwd>
<kwd lng="es"><![CDATA[Anormalidades de los dientes]]></kwd>
<kwd lng="es"><![CDATA[Reportes del caso]]></kwd>
<kwd lng="es"><![CDATA[Revisión sistemática]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Cheon]]></surname>
<given-names><![CDATA[C. K.]]></given-names>
</name>
<name>
<surname><![CDATA[Ko]]></surname>
<given-names><![CDATA[J. M.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Kabuki syndrome: clinical and molecular characteristics.]]></article-title>
<source><![CDATA[Korean J Pediatr]]></source>
<year>2015</year>
<volume>58</volume>
<numero>9</numero>
<issue>9</issue>
<page-range>317-24</page-range></nlm-citation>
</ref>
<ref id="B2">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Shangguan]]></surname>
<given-names><![CDATA[H.]]></given-names>
</name>
<name>
<surname><![CDATA[Su]]></surname>
<given-names><![CDATA[C.]]></given-names>
</name>
<name>
<surname><![CDATA[Ouyang]]></surname>
<given-names><![CDATA[Q.]]></given-names>
</name>
<name>
<surname><![CDATA[Cao]]></surname>
<given-names><![CDATA[B.]]></given-names>
</name>
<name>
<surname><![CDATA[Wang]]></surname>
<given-names><![CDATA[J.]]></given-names>
</name>
<name>
<surname><![CDATA[Gong]]></surname>
<given-names><![CDATA[C.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Kabuki syndrome: novel pathogenic variants, new phenotypes and review of literature]]></article-title>
<source><![CDATA[Orphanet J Rare Dis]]></source>
<year>2019</year>
<volume>14</volume>
<page-range>255</page-range></nlm-citation>
</ref>
<ref id="B3">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Geneviève]]></surname>
<given-names><![CDATA[D.]]></given-names>
</name>
<name>
<surname><![CDATA[Amiel]]></surname>
<given-names><![CDATA[J.]]></given-names>
</name>
<name>
<surname><![CDATA[Viot]]></surname>
<given-names><![CDATA[G.]]></given-names>
</name>
<name>
<surname><![CDATA[Le Merrer]]></surname>
<given-names><![CDATA[M.]]></given-names>
</name>
<name>
<surname><![CDATA[Sanlaville]]></surname>
<given-names><![CDATA[D.]]></given-names>
</name>
<name>
<surname><![CDATA[Urtizberea]]></surname>
<given-names><![CDATA[A.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Atypical findings in Kabuki syndrome: report of 8 patients in a series of 20 and review of the literature]]></article-title>
<source><![CDATA[Am J Med Genet A]]></source>
<year>2004</year>
<volume>129</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>64-8</page-range></nlm-citation>
</ref>
<ref id="B4">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Sattur]]></surname>
<given-names><![CDATA[A.]]></given-names>
</name>
<name>
<surname><![CDATA[Deshmukh]]></surname>
<given-names><![CDATA[P. K.]]></given-names>
</name>
<name>
<surname><![CDATA[Abrahim]]></surname>
<given-names><![CDATA[L.]]></given-names>
</name>
<name>
<surname><![CDATA[Naikmasur]]></surname>
<given-names><![CDATA[V. G.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Kabuki Make-up Syndrome- A Case Report with Electromyographic study]]></article-title>
<source><![CDATA[J Clin Diagn Res]]></source>
<year>2014</year>
<volume>8</volume>
<numero>11</numero>
<issue>11</issue>
<page-range>ZD03-6</page-range></nlm-citation>
</ref>
<ref id="B5">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Matsumoto]]></surname>
<given-names><![CDATA[N.]]></given-names>
</name>
<name>
<surname><![CDATA[Niikawa]]></surname>
<given-names><![CDATA[N.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Kabuki make- up syndrome: a review]]></article-title>
<source><![CDATA[Am J Med Genet C Semin Med Genet]]></source>
<year>2003</year>
<volume>117</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>57-65</page-range></nlm-citation>
</ref>
<ref id="B6">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Adam]]></surname>
<given-names><![CDATA[M. P.]]></given-names>
</name>
<name>
<surname><![CDATA[Hudgins]]></surname>
<given-names><![CDATA[L.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Kabuki syndrome: a review]]></article-title>
<source><![CDATA[Clin Genet]]></source>
<year>2005</year>
<volume>67</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>209-19</page-range></nlm-citation>
</ref>
<ref id="B7">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Galvão]]></surname>
<given-names><![CDATA[T. F.]]></given-names>
</name>
<name>
<surname><![CDATA[Pansani]]></surname>
<given-names><![CDATA[T. S. A.]]></given-names>
</name>
<name>
<surname><![CDATA[Harrad]]></surname>
<given-names><![CDATA[D.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Principais itens para relatar Revisões sistemáticas e Meta-análises:Arecomendação PRISMA]]></article-title>
<source><![CDATA[Epidemiol. Serv. Saúde]]></source>
<year>2015</year>
<volume>24</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>335-42</page-range></nlm-citation>
</ref>
<ref id="B8">
<nlm-citation citation-type="">
<collab>The Joanna Briggs Institute (JBI)</collab>
<source><![CDATA[Critical Appraisal Checklist for Case Reports]]></source>
<year>2017</year>
</nlm-citation>
</ref>
<ref id="B9">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Santos]]></surname>
<given-names><![CDATA[C. N.]]></given-names>
</name>
<name>
<surname><![CDATA[Cardoso]]></surname>
<given-names><![CDATA[M. C. A. C.]]></given-names>
</name>
<name>
<surname><![CDATA[Turrioni]]></surname>
<given-names><![CDATA[A. P.]]></given-names>
</name>
<name>
<surname><![CDATA[Santo]]></surname>
<given-names><![CDATA[A. S. M.]]></given-names>
</name>
<name>
<surname><![CDATA[Paranhos]]></surname>
<given-names><![CDATA[L. R.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Talon cusp in the temporary dentition of a patient with Kabuki syndrome: Case report with a two-year follow-up]]></article-title>
<source><![CDATA[Spec Care Dentist]]></source>
<year>2019</year>
<volume>39</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>624-30</page-range></nlm-citation>
</ref>
<ref id="B10">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Silva-Andrade]]></surname>
<given-names><![CDATA[N.]]></given-names>
</name>
<name>
<surname><![CDATA[López-Ortega]]></surname>
<given-names><![CDATA[K.]]></given-names>
</name>
<name>
<surname><![CDATA[Gallottini]]></surname>
<given-names><![CDATA[M.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Orofacial features and medical profile of eight individuals with Kabuki syndrome]]></article-title>
<source><![CDATA[Med Oral Patol Oral Cir Bucal]]></source>
<year>2019</year>
<volume>24</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>e630-5</page-range></nlm-citation>
</ref>
<ref id="B11">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Tuna]]></surname>
<given-names><![CDATA[E. B.]]></given-names>
</name>
<name>
<surname><![CDATA[Mar&#351;an]]></surname>
<given-names><![CDATA[G.]]></given-names>
</name>
<name>
<surname><![CDATA[Gençay]]></surname>
<given-names><![CDATA[K.]]></given-names>
</name>
<name>
<surname><![CDATA[Seymen]]></surname>
<given-names><![CDATA[F.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Craniofacial and dental characteristics of Kabuki syndrome: nine years cephalometric follow-up]]></article-title>
<source><![CDATA[J Clin Pediatr Dent]]></source>
<year>2012</year>
<volume>36</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>393-400</page-range></nlm-citation>
</ref>
<ref id="B12">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Teixeira]]></surname>
<given-names><![CDATA[C. S.]]></given-names>
</name>
<name>
<surname><![CDATA[Silva]]></surname>
<given-names><![CDATA[C. R.]]></given-names>
</name>
<name>
<surname><![CDATA[Honjo]]></surname>
<given-names><![CDATA[R. S.]]></given-names>
</name>
<name>
<surname><![CDATA[Bertola]]></surname>
<given-names><![CDATA[D. R.]]></given-names>
</name>
<name>
<surname><![CDATA[Albano]]></surname>
<given-names><![CDATA[L. M.]]></given-names>
</name>
<name>
<surname><![CDATA[Kim]]></surname>
<given-names><![CDATA[C. A.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Dental evaluation of Kabuki syndrome patients]]></article-title>
<source><![CDATA[Cleft Palate Craniofac J.]]></source>
<year>2009</year>
<volume>46</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>668-73</page-range></nlm-citation>
</ref>
<ref id="B13">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Rocha]]></surname>
<given-names><![CDATA[C. T.]]></given-names>
</name>
<name>
<surname><![CDATA[Peixoto]]></surname>
<given-names><![CDATA[I. T.]]></given-names>
</name>
<name>
<surname><![CDATA[Fernandes]]></surname>
<given-names><![CDATA[P. M.]]></given-names>
</name>
<name>
<surname><![CDATA[Torres]]></surname>
<given-names><![CDATA[C. P.]]></given-names>
</name>
<name>
<surname><![CDATA[de Queiroz]]></surname>
<given-names><![CDATA[A. M.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Dental findings in Kabuki make-up syndrome: a case report]]></article-title>
<source><![CDATA[Spec Care Dentist]]></source>
<year>2008</year>
<volume>28</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>53-7</page-range></nlm-citation>
</ref>
<ref id="B14">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[dos Santos]]></surname>
<given-names><![CDATA[B. M.]]></given-names>
</name>
<name>
<surname><![CDATA[Ribeiro]]></surname>
<given-names><![CDATA[R. R.]]></given-names>
</name>
<name>
<surname><![CDATA[Stuani]]></surname>
<given-names><![CDATA[A. S.]]></given-names>
</name>
<name>
<surname><![CDATA[de Paula e Silva]]></surname>
<given-names><![CDATA[F. W.]]></given-names>
</name>
<name>
<surname><![CDATA[de Queiroz]]></surname>
<given-names><![CDATA[A. M.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Kabuki make-up (Niikawa-Kuroki) syndrome: dental and craniofacial findings in a Brazilian child]]></article-title>
<source><![CDATA[Braz Dent J.]]></source>
<year>2006</year>
<volume>17</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>249-54</page-range></nlm-citation>
</ref>
<ref id="B15">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Atar]]></surname>
<given-names><![CDATA[M.]]></given-names>
</name>
<name>
<surname><![CDATA[Lee]]></surname>
<given-names><![CDATA[W.]]></given-names>
</name>
<name>
<surname><![CDATA[O'Donnell]]></surname>
<given-names><![CDATA[D.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Kabuki syndrome: oral and general features seen in a 2-year-old Chinese boy]]></article-title>
<source><![CDATA[Int J Paediatr Dent]]></source>
<year>2006</year>
<volume>16</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>222-6</page-range></nlm-citation>
</ref>
<ref id="B16">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Schrander-Stumpel]]></surname>
<given-names><![CDATA[C. T.]]></given-names>
</name>
<name>
<surname><![CDATA[Spruyt]]></surname>
<given-names><![CDATA[L.]]></given-names>
</name>
<name>
<surname><![CDATA[Curfs]]></surname>
<given-names><![CDATA[L. M.]]></given-names>
</name>
<name>
<surname><![CDATA[Defloor]]></surname>
<given-names><![CDATA[T.]]></given-names>
</name>
<name>
<surname><![CDATA[Schrander]]></surname>
<given-names><![CDATA[J. J.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Kabuki syndrome: Clinical data in 20 patients, literature review, and further guidelines for preventive management]]></article-title>
<source><![CDATA[Am J Med Genet A.]]></source>
<year>2005</year>
<volume>132</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>234-43</page-range></nlm-citation>
</ref>
<ref id="B17">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Shalev]]></surname>
<given-names><![CDATA[S. A.]]></given-names>
</name>
<name>
<surname><![CDATA[Clarke]]></surname>
<given-names><![CDATA[L. A.]]></given-names>
</name>
<name>
<surname><![CDATA[Koehn]]></surname>
<given-names><![CDATA[D.]]></given-names>
</name>
<name>
<surname><![CDATA[Langlois]]></surname>
<given-names><![CDATA[S.]]></given-names>
</name>
<name>
<surname><![CDATA[Zackai]]></surname>
<given-names><![CDATA[E. H.]]></given-names>
</name>
<name>
<surname><![CDATA[Hall]]></surname>
<given-names><![CDATA[J. G.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Long-term follow-up of three individuals with Kabuki syndrome]]></article-title>
<source><![CDATA[Am J Med Genet A]]></source>
<year>2004</year>
<volume>125</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>191-200</page-range></nlm-citation>
</ref>
<ref id="B18">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Petzold]]></surname>
<given-names><![CDATA[D.]]></given-names>
</name>
<name>
<surname><![CDATA[Kratzsch]]></surname>
<given-names><![CDATA[E.]]></given-names>
</name>
<name>
<surname><![CDATA[Opitz]]></surname>
<given-names><![CDATA[Ch.]]></given-names>
</name>
<name>
<surname><![CDATA[Tinschert]]></surname>
<given-names><![CDATA[S.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[The Kabuki syndrome: four patients with oral abnormalities]]></article-title>
<source><![CDATA[Eur J Orthod]]></source>
<year>2003</year>
<volume>25</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>13-9</page-range></nlm-citation>
</ref>
<ref id="B19">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Mhanni]]></surname>
<given-names><![CDATA[A. A.]]></given-names>
</name>
<name>
<surname><![CDATA[Cross]]></surname>
<given-names><![CDATA[H. G.]]></given-names>
</name>
<name>
<surname><![CDATA[Chudley]]></surname>
<given-names><![CDATA[A. E.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Kabuki syndrome: description of dental findings in 8 patients]]></article-title>
<source><![CDATA[Clin Genet]]></source>
<year>1999</year>
<volume>56</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>154-7</page-range></nlm-citation>
</ref>
<ref id="B20">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Elmubarak]]></surname>
<given-names><![CDATA[N. A.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Genetic Risk of Talon Cusp: Talon Cusp in Five Siblings]]></article-title>
<source><![CDATA[Case Rep Dent]]></source>
<year>2019</year>
</nlm-citation>
</ref>
<ref id="B21">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Chotta]]></surname>
<given-names><![CDATA[N. A.]]></given-names>
</name>
<name>
<surname><![CDATA[Mgongo]]></surname>
<given-names><![CDATA[M.]]></given-names>
</name>
<name>
<surname><![CDATA[Msuya]]></surname>
<given-names><![CDATA[S. E.]]></given-names>
</name>
<name>
<surname><![CDATA[Nyombi]]></surname>
<given-names><![CDATA[B. M.]]></given-names>
</name>
<name>
<surname><![CDATA[Uriyo]]></surname>
<given-names><![CDATA[J. G.]]></given-names>
</name>
<name>
<surname><![CDATA[Stray-Pedersen]]></surname>
<given-names><![CDATA[B.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Prevalence and factors associated with HIV and syphilis infection among children aged 0-36 months in Kilimanjaro, Tanzania: a community-based cross-sectional study]]></article-title>
<source><![CDATA[Trop Med Health]]></source>
<year>2019</year>
<volume>47</volume>
<page-range>53</page-range></nlm-citation>
</ref>
<ref id="B22">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[MacDonald]]></surname>
<given-names><![CDATA[D.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Taurodontism]]></article-title>
<source><![CDATA[Oral Radiol]]></source>
<year>2019</year>
</nlm-citation>
</ref>
<ref id="B23">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Giambersio]]></surname>
<given-names><![CDATA[E.]]></given-names>
</name>
<name>
<surname><![CDATA[Barile]]></surname>
<given-names><![CDATA[V.]]></given-names>
</name>
<name>
<surname><![CDATA[Giambersio]]></surname>
<given-names><![CDATA[A. M.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Klinefelter's syndrome and taurodontism]]></article-title>
<source><![CDATA[Arch Ital Urol Androl]]></source>
<year>2019</year>
<volume>91</volume>
<numero>2</numero>
<issue>2</issue>
</nlm-citation>
</ref>
<ref id="B24">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Haghanifar]]></surname>
<given-names><![CDATA[S.]]></given-names>
</name>
<name>
<surname><![CDATA[Moudi]]></surname>
<given-names><![CDATA[E.]]></given-names>
</name>
<name>
<surname><![CDATA[Abesi]]></surname>
<given-names><![CDATA[F.]]></given-names>
</name>
<name>
<surname><![CDATA[Kheirkhah]]></surname>
<given-names><![CDATA[F.]]></given-names>
</name>
<name>
<surname><![CDATA[Arbabzadegan]]></surname>
<given-names><![CDATA[N.]]></given-names>
</name>
<name>
<surname><![CDATA[Bijani]]></surname>
<given-names><![CDATA[A.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Radiographic Evaluation of Dental Anomaly Prevalence in a Selected Iranian Population]]></article-title>
<source><![CDATA[J Dent (Shiraz)]]></source>
<year>2019</year>
<volume>20</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>90-4</page-range></nlm-citation>
</ref>
<ref id="B25">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Choi]]></surname>
<given-names><![CDATA[S. J.]]></given-names>
</name>
<name>
<surname><![CDATA[Lee]]></surname>
<given-names><![CDATA[J. W.]]></given-names>
</name>
<name>
<surname><![CDATA[Song]]></surname>
<given-names><![CDATA[J. H.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Dental anomaly patterns associated with tooth agenesis]]></article-title>
<source><![CDATA[Acta Odontol Scand]]></source>
<year>2017</year>
<volume>75</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>161-5</page-range></nlm-citation>
</ref>
<ref id="B26">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Al-Abdallah]]></surname>
<given-names><![CDATA[M.]]></given-names>
</name>
<name>
<surname><![CDATA[AlHadidi]]></surname>
<given-names><![CDATA[A.]]></given-names>
</name>
<name>
<surname><![CDATA[Hammad]]></surname>
<given-names><![CDATA[M.]]></given-names>
</name>
<name>
<surname><![CDATA[Al-Ahmad]]></surname>
<given-names><![CDATA[H.]]></given-names>
</name>
<name>
<surname><![CDATA[Saleh]]></surname>
<given-names><![CDATA[R.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Prevalence and distribution of dental anomalies: a comparison between maxillary and mandibular tooth agenesis]]></article-title>
<source><![CDATA[Am J Orthod Dentofacial Orthop]]></source>
<year>2015</year>
<volume>148</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>793-8</page-range></nlm-citation>
</ref>
<ref id="B27">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Adam]]></surname>
<given-names><![CDATA[M. P.]]></given-names>
</name>
<name>
<surname><![CDATA[Banka]]></surname>
<given-names><![CDATA[S.]]></given-names>
</name>
<name>
<surname><![CDATA[Bjornsson]]></surname>
<given-names><![CDATA[H. T.]]></given-names>
</name>
<name>
<surname><![CDATA[Bodamer]]></surname>
<given-names><![CDATA[O.]]></given-names>
</name>
<name>
<surname><![CDATA[Chudley]]></surname>
<given-names><![CDATA[A. E.]]></given-names>
</name>
<name>
<surname><![CDATA[Harris]]></surname>
<given-names><![CDATA[J.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Kabuki syndrome: international consensus diagnostic criteria]]></article-title>
<source><![CDATA[J Med Genet]]></source>
<year>2019</year>
<volume>56</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>89-95</page-range></nlm-citation>
</ref>
<ref id="B28">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Wang]]></surname>
<given-names><![CDATA[Y.]]></given-names>
</name>
<name>
<surname><![CDATA[Li]]></surname>
<given-names><![CDATA[N.]]></given-names>
</name>
<name>
<surname><![CDATA[Su]]></surname>
<given-names><![CDATA[Z.]]></given-names>
</name>
<name>
<surname><![CDATA[Xu]]></surname>
<given-names><![CDATA[Y.]]></given-names>
</name>
<name>
<surname><![CDATA[Liu]]></surname>
<given-names><![CDATA[S.]]></given-names>
</name>
<name>
<surname><![CDATA[Chen]]></surname>
<given-names><![CDATA[Y.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[The phenotypic spectrum of Kabuki syndrome in patients of Chinese descent: A case series]]></article-title>
<source><![CDATA[Am J Med Genet A]]></source>
<year>2019</year>
</nlm-citation>
</ref>
<ref id="B29">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Ruault]]></surname>
<given-names><![CDATA[V.]]></given-names>
</name>
<name>
<surname><![CDATA[Corsini]]></surname>
<given-names><![CDATA[C.]]></given-names>
</name>
<name>
<surname><![CDATA[Duflos]]></surname>
<given-names><![CDATA[C.]]></given-names>
</name>
<name>
<surname><![CDATA[Akouete]]></surname>
<given-names><![CDATA[S.]]></given-names>
</name>
<name>
<surname><![CDATA[Georgescu]]></surname>
<given-names><![CDATA[V.]]></given-names>
</name>
<name>
<surname><![CDATA[Abaji]]></surname>
<given-names><![CDATA[M.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Growth charts in Kabuki syndrome 1]]></article-title>
<source><![CDATA[Am J Med Genet A]]></source>
<year>2019</year>
</nlm-citation>
</ref>
<ref id="B30">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Wang]]></surname>
<given-names><![CDATA[Y. R.]]></given-names>
</name>
<name>
<surname><![CDATA[Xu]]></surname>
<given-names><![CDATA[N. X.]]></given-names>
</name>
<name>
<surname><![CDATA[Wang]]></surname>
<given-names><![CDATA[J.]]></given-names>
</name>
<name>
<surname><![CDATA[Wang]]></surname>
<given-names><![CDATA[X. M.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Kabuki syndrome: review of the clinical features, diagnosis and epigenetic mechanisms.]]></article-title>
<source><![CDATA[World J Pediatr.]]></source>
<year>2019</year>
<volume>15</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>528-35</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
