<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1409-4568</journal-id>
<journal-title><![CDATA[Enfermería Actual de Costa Rica]]></journal-title>
<abbrev-journal-title><![CDATA[Enfermería Actual de Costa Rica]]></abbrev-journal-title>
<issn>1409-4568</issn>
<publisher>
<publisher-name><![CDATA[Universidad de Costa Rica ]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1409-45682020000200027</article-id>
<article-id pub-id-type="doi">10.15517/revenf.v0i39.38784</article-id>
<title-group>
<article-title xml:lang="pt"><![CDATA[O enfrentamento do tratamento da doença falciforme: desafios e perspectivas vivenciadas pela família]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<given-names><![CDATA[Rhalliete Souza]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cunha]]></surname>
<given-names><![CDATA[Brenda do Socorro Gomes da]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Oliveira]]></surname>
<given-names><![CDATA[Elenilda Farias de]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Araújo]]></surname>
<given-names><![CDATA[Ana Joyce]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Jesus]]></surname>
<given-names><![CDATA[Viviane Silva de]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Nascimento]]></surname>
<given-names><![CDATA[Ohana Cunha do]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidade Federal do Recôncavo da Bahia  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Brazil</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidade Federal Fluminense Instituição de Ensino FAM ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Brazil</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Faculdade Adventista da Bahia  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Brasil</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Faculdade Adventista da Bahia  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Brasil</country>
</aff>
<aff id="Af5">
<institution><![CDATA[,Universidade Federal da Bahia e Pitágoras Medicina Eunápolis  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
</aff>
<aff id="Af6">
<institution><![CDATA[,Universidade Estadual de Feira de Santana e Universidade Salvador  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Brazil</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<numero>39</numero>
<fpage>27</fpage>
<lpage>37</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_arttext&amp;pid=S1409-45682020000200027&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_abstract&amp;pid=S1409-45682020000200027&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_pdf&amp;pid=S1409-45682020000200027&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo A doença falciforme é um distúrbio hemolítico grave causado por mutação genética, o que ocasiona a produção da hemoglobina S mutante. Este estudo teve como objetivo compreender a forma de enfrentamento dos familiares frente ao tratamento da doença falciforme. Trata-se de uma pesquisa de campo, com uma abordagem qualitativa. O estudo utilizou como base entrevistas realizadas com mães de crianças e adolescentes com doença falciforme assistidas pelo Centro de Referência de uma cidade do estado da Bahia, Brasil, no ano de 2017. Com base nas informações coletadas foi possível perceber que pessoas com anemia falciforme, durante boa parte da vida, requerem tratamentos específicos que poderão ser executados por elas mesmas ou com ajuda e encorajamento de outras pessoas, em geral familiares. É muito importante refletir sobre a efetividade do tratamento não só do ponto de vista técnico como também sob a ótica do paciente, de sua família e da sociedade.]]></p></abstract>
<abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen La enfermedad de falciforme es un trastorno hemolítico grave causado por la mutación genética, lo que ocasiona la producción de la hemoglobina S mutante. Este estudio tuvo como objetivo comprender la forma de enfrentamiento de los familiares frente al tratamiento de la enfermedad falciforme. Se trata de una investigación de campo, con un enfoque cualitativo. El estudio utilizó como base entrevistas realizadas con madres de niños y adolescentes con enfermedad falciforme asistidas por el Centro de Referencia de una ciudad del estado de Bahía, Brasil, en el año 2017. Con base en las informaciones recogidas fue posible percibir que personas con anemia falciforme durante buena parte de la vida, requieren tratamientos específicos que pueden ser ejecutados por ellas mismas o con ayuda y atención de otras personas, en general familiares. Es muy importante reflexionar sobre la efectividad del tratamiento no sólo desde el punto de vista técnico, sino también, bajo la óptica del paciente, de su familia y de la sociedad.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Sickle cell disease is a serious hemolytic disorder caused by genetic mutation, which causes production of the mutant hemoglobin S. The objective of this paper was to understand how family members cope with the treatment of sickle cell disease. This is a field research with a qualitative approach. The study used as a basis interviews conducted with mothers of children and adolescents with sickle cell disease assisted by the Reference Center of a city in the state of Bahia, Brazil, in the year 2017. Based on the information collected it was possible to perceive that people with sickle cell anemia during good require specific treatments that may be performed by themselves or with the help and encouragement of others, usually family members. It is very important to reflect on the effectiveness of treatment not only from the technical point of view but also from the point of view of the patient, his family and society]]></p></abstract>
<kwd-group>
<kwd lng="pt"><![CDATA[Anemia-Falciforme]]></kwd>
<kwd lng="pt"><![CDATA[Dor]]></kwd>
<kwd lng="pt"><![CDATA[Tratamento.]]></kwd>
<kwd lng="es"><![CDATA[Anemia-de-Células-Falciformes]]></kwd>
<kwd lng="es"><![CDATA[Dolor]]></kwd>
<kwd lng="es"><![CDATA[Tratamiento.]]></kwd>
<kwd lng="en"><![CDATA[Pain]]></kwd>
<kwd lng="en"><![CDATA[Sickle-Cell-Disease]]></kwd>
<kwd lng="en"><![CDATA[Treatment.]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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<surname><![CDATA[Ferreira]]></surname>
<given-names><![CDATA[SL.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Conhecimento de enfermeiras sobre educação para o autocuidado na anemia falciforme.]]></article-title>
<source><![CDATA[Revista Baiana de Enfermagem]]></source>
<year>2013</year>
<volume>27</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>4-12.</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
