<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1409-0015</journal-id>
<journal-title><![CDATA[Medicina Legal de Costa Rica]]></journal-title>
<abbrev-journal-title><![CDATA[Med. leg. Costa Rica]]></abbrev-journal-title>
<issn>1409-0015</issn>
<publisher>
<publisher-name><![CDATA[Asociación Costarricense de Medicina Forense]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1409-00152019000100127</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Malformaciones cardíacas causantes de muerte súbita en adulto]]></article-title>
<article-title xml:lang="en"><![CDATA[Cardiac malformations causing sudden death in adults]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cortés Valerio]]></surname>
<given-names><![CDATA[Asdrúbal]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cortés Bejarano]]></surname>
<given-names><![CDATA[Federico]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cortés Morales]]></surname>
<given-names><![CDATA[Estefany]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Duarte Núñez]]></surname>
<given-names><![CDATA[Daniela]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Quesada Campos]]></surname>
<given-names><![CDATA[Jazmín]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Cardiología  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Costa Rica</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Médico(a) General  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Costa Rica</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2019</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2019</year>
</pub-date>
<volume>36</volume>
<numero>1</numero>
<fpage>127</fpage>
<lpage>134</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_arttext&amp;pid=S1409-00152019000100127&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_abstract&amp;pid=S1409-00152019000100127&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_pdf&amp;pid=S1409-00152019000100127&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen La muerte súbita cardiaca se define como la muerte que ocurre dentro de una hora después de inicio de síntomas en los casos presenciados y en los no presenciados dentro de las últimas 24 horas de haberse visto con vida. Su incidencia anual en el mundo ronda entre 4-5 millones de casos. Aproximadamente un 90-95% de las víctimas de muerte súbita cardíaca sufren una cardiopatía estructural. Siendo la cardiopatía isquémica la causa principal en mayores de 35 años y las afectaciones congénitas y hereditarias en adultos jóvenes entre 18-35 años. La etiología de la muerte súbita cardíaca se puede clasificar en coronariopatías, miocardiopatías, cardiopatías congénitas, enfermedades eléctricas hereditarias y cardiopatías adquiridas. Siendo la aterosclerosis y la miocardiopatía dilatada las más prevalentes y de las cardiopatías congénitas la que tiene mayor mortalidad por muerte súbita cardíaca es la coartación de aorta. Múltiples mecanismos pueden derivar en muerte súbita cardíaca como fibrilación ventricular, taquicardia ventricular polimorfa y actividad eléctrica sin pulso. Sin embargo, en la actualidad la muerte súbita cardíaca continúa siendo un reto en la salud pública, tanto el diagnóstico como el tratamiento oportuno. Mediante la prevención de factores de riesgo modificables y con el control adecuado de los no modificables, así como la optimización de la terapéutica, se podrá reducir la incidencia de muerte súbita cardíaca.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Sudden cardiac death is defined as death that occurs within one hour after the onset of symptoms in the presence and not witnessed cases within the last 24 hours of having seen life. Its annual incidence in the world is between 4-5 million cases. Approximately 90-95% of victims of sudden cardiac death suffered from structural heart disease. Ischemic heart disease is the main cause in people older than 35 years and the congenital and hereditary affectations in young adults between 18-35 years. The etiology of sudden cardiac death can be classified as coronary artery disease, cardiomyopathy, congenital heart disease, hereditary diseases and acquired heart disease. Being atherosclerosis and dilated cardiomyopathy the most frequent and congenital cardiopathies, the one with the highest mortality due to sudden cardiac death is the coarctation of the aorta. Multiple mechanisms can lead to sudden cardiac death such as ventricular fibrillation, polymorphic ventricular tachycardia and pulseless electrical activity. However, at the right time. Through the prevention of modifiable risk factors and with the adequate control of the no -modifiable ones, as well as the optimization of therapeutics, the incidence of sudden cardiac death can be reduced.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Muerte súbita cardiaca]]></kwd>
<kwd lng="es"><![CDATA[malformaciones cardiacas]]></kwd>
<kwd lng="es"><![CDATA[cardiomiopatía]]></kwd>
<kwd lng="es"><![CDATA[enfermedad cardiaca congénita en el adulto]]></kwd>
<kwd lng="en"><![CDATA[Sudden cardiac death]]></kwd>
<kwd lng="en"><![CDATA[cardiac malformations]]></kwd>
<kwd lng="en"><![CDATA[cardiomyopathy]]></kwd>
<kwd lng="en"><![CDATA[congenital heart disease in adults]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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