<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0001-6002</journal-id>
<journal-title><![CDATA[Acta Médica Costarricense]]></journal-title>
<abbrev-journal-title><![CDATA[Acta méd. costarric]]></abbrev-journal-title>
<issn>0001-6002</issn>
<publisher>
<publisher-name><![CDATA[Colegio de Médicos y Cirujanos de Costa Rica]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0001-60022018000400172</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Supervivencia de los niños nacidos con cardiopatías congénitas en Costa Rica: estudio retrospectivo de la cohorte de nacimientos 2006-2007]]></article-title>
<article-title xml:lang="en"><![CDATA[Survival of children born with congenital heart defects in Costa Rica: a retrospective study of the birth cohort 2006-2007]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Benavides Lara]]></surname>
<given-names><![CDATA[Adriana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Vargas-Leitón]]></surname>
<given-names><![CDATA[Bernardo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Faerron-Angel]]></surname>
<given-names><![CDATA[Jorge E]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Costarricense de Enseñanza e Investigación en Nutrición y Salud Centro de Registro de Enfermedades Congénitas ]]></institution>
<addr-line><![CDATA[Cartago ]]></addr-line>
<country>Costa Rica</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad Nacional Posgrado Regional en Ciencias Veterinarias Tropicales ]]></institution>
<addr-line><![CDATA[Heredia ]]></addr-line>
<country>Costa Rica</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Caja Costarricense del Seguro Social Departamento de Cardiología, HNN &#8220;Dr. Carlos Sáenz Herrera&#8221; ]]></institution>
<addr-line><![CDATA[San José ]]></addr-line>
<country>Costa Rica</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2018</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2018</year>
</pub-date>
<volume>60</volume>
<numero>4</numero>
<fpage>172</fpage>
<lpage>181</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_arttext&amp;pid=S0001-60022018000400172&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_abstract&amp;pid=S0001-60022018000400172&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.sa.cr/scielo.php?script=sci_pdf&amp;pid=S0001-60022018000400172&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen Justificación: alrededor del mundo las cardiopatías congénitas ocupan las primeras causas de mortalidad infantil. En Costa Rica son el grupo de defectos congénitos más frecuentes, con una prevalencia de 6 x 1000 nacimientos (IC95 % 5 -7 x 1000 nacimientos), que representan cerca del 13 % de la mortalidad infantil. El objetivo del estudio fue analizar la supervivencia a cinco años de edad de los niños nacidos con defectos cardiacos en Costa Rica.  Métodos:  Se analizó una cohorte retrospectiva de 543 niños nacidos con cardiopatías congénitas entre enero de 2006 y junio de 2007 en Costa Rica; utilizando los registros médicos y la base nacional de defunciones se brindó un seguimiento mínimo de 5 años en todos los casos. Se obtuvo estimados de supervivencia de Kaplan-Meier al mes, año y cinco años de vida, y se evaluaron factores pronóstico empleando el modelo de riesgos proporcionales de Cox. Se estimaron riesgos relativos crudos y ajustados con su respectivo intervalo de confianza del 95 %.  Resultados:  La prevalencia de cardiopatías congénitas fue de 5,14 por 1000 nacimientos (IC95 % 4,73-5,60; n: 543) para el período de estudio. La mortalidad fue del 27,9 % (IC 95 % = 24,21- 31,73; n: 152). La supervivencia acumulada al año y cinco años fue del 76,1 % y el 72,4 %, respectivamente, frente al 99,1 % y 98,8 % sobrevivencia de la cohorte de nacimientos nacional (con y sin cardiopatía) de la misma edad. La edad temprana al diagnóstico, severidad, cardiopatías congénitas múltiples y la asociación de defectos congénitos mayores se asociaron significativamente (p&#8804;0,05) a una menor probabilidad de supervivencia.  Conclusiones:  La cohorte de niños con cardiopatías congénitas estudiada presentó una alta mortalidad al año y cinco años. El peor pronóstico de supervivencia fue para aquellos que necesitaban una cirugía cardíaca a temprana edad.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Background: Around the world, congenital heart defects occupy the first causes of infant mortality. In Costa Rica heart malformations are the most frequent group of birth defects, with a prevalence of 6 x 1000 births (95% CI 5-7 x 1000 births). They represent about 13% of infant mortality and are. the leading cause of death due to birth defects. The objective of this study is to analyze the survival of children with CC in Costa Rica.  Methods: A retrospective cohort of 543 children born with CC between January 2006 and June 2007 in Costa Rica was analyzed. Using medical records and the national database of deaths, a minimum follow-up of 5 years was given in all cases. Kaplan-Meier survival estimates were obtained at month, year and five years of life. Prognostic factors were assessed using the Cox proportional hazards model. Raw and adjusted relative risks were estimated with their respective 95% confidence interval.  Results: The prevalence of CC was 5.14 per 1000 births (95% CI: 4.73-5.60; n: 543) for the study period. Mortality was 27.9% (95% CI: 24.21-31.73; n: 152). Cumulative survival at one year and five years was 76.1% and 72.4%, respectively, compared to 99.1% and 98.8% of survival in the same national birth cohort (with and without CC), at the same age. Early age at diagnosis, severity, multiple CC and the association of major BD were significantly associated (p&#8804;0.05) with a lower probability of survival.  Conclusions: The cohort of children with congenital heart disease studied had a high mortality rate at one year and five years. The worst prognosis of survival was for those who needed cardiac surgery at an early age.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[cardiopatías congénitas]]></kwd>
<kwd lng="es"><![CDATA[mortalidad]]></kwd>
<kwd lng="es"><![CDATA[supervivencia]]></kwd>
<kwd lng="es"><![CDATA[epidemiología]]></kwd>
<kwd lng="en"><![CDATA[congenital heart defects]]></kwd>
<kwd lng="en"><![CDATA[mortality]]></kwd>
<kwd lng="en"><![CDATA[survival]]></kwd>
<kwd lng="en"><![CDATA[epidemiology]]></kwd>
</kwd-group>
</article-meta>
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