Services on Demand
Journal
Article
Indicators
- Cited by SciELO
- Access statistics
Related links
- Similars in SciELO
Share
Odovtos International Journal of Dental Sciences
On-line version ISSN 2215-3411Print version ISSN 1659-1046
Abstract
KESKIN, Gül and TEK, Gün B.. Dental Rehabilitation of a Rare Hallermann-Streiff Syndrome with Olygodontia: A Case Report. Odovtos [online]. 2020, vol.22, n.3, pp.54-58. ISSN 2215-3411. http://dx.doi.org/10.15517/ijds.2020.42072.
Hallermann-Streiff syndrome (HSS) is a rare oculomandibulofacial discephaly with hypotrichosis that occurs as a sporadic mutation. It is characterized by abnormal findings especially in head and face. Dental anomalies occur in 50-80% of the patients. In this case report, facial-oral findings and the existing dental anomalies of the syndrome in a 6-year-old male patient diagnosed with HSS were identified. Dental rehabilitation and a 12-month follow-up of the patient were reported. Each case presented with this rare syndrome may contribute to the literature to determine the prognosis of the disease and to take protective and preventive measures.
Keywords : Dental anomalies; Hallermann-Streiff syndrome; Tooth agenesis; Primary dentition; Nance appliance; Pediatric dentistry.