Resumen

VARELA, Wilson  y  BRIZUELA, Jorge. Miocardiopatía no-compacta biventricular. Rev. costarric. cardiol [online]. 2016, vol.18, n.1-2, pp.30-36. ISSN 1409-4142.

Left ventricular non-compaction cardiomyopathy (LVNC) is a rare condition associated with high morbidity and mortality due to malignant arrhythmias, systemic thrombotic embolism and heart failure. LVNC is thought to be caused by an arrest in the normal myocardial compaction process during early intrauterine life. Normal compaction of the embryonic myocardium proceeds from the epicardium to the endocardium and from the base of the heart to the apex. During early embryogenesis, the heart consists of loose mesh of muscle fibers that will gradually become compressed, this process is more pronounced in the left ventricle. An insufficient compaction of the myocardium will result in multiple prominent ventricular trabeculations and inter trabecular recesses that will predominantly affect the ventricular endocardium and the apex of the LV. Non-compaction of the left ventricular myocardium can occur in isolation, or in association with other conditions such as congenital heart defects (CHDs), genetic syndromes, and/or neuromuscular disorders, among others.

We report the case of a 42 year-old male patient with dyspnea and ECG findings of left bundle branch block, who was referred to the Cardiology Department for evaluation. The echocardiogram performed revealed increased trabeculations and deep intertrabecular recesses in the endocardial wall of both ventricles.

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