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Medicina Legal de Costa Rica
versão On-line ISSN 2215-5287versão impressa ISSN 1409-0015
Resumo
GARRO DONINI, Alessio. Drenaje Pulmonar Anómalo Total con Drenaje de Pulmonares a Vena Porta. Med. leg. Costa Rica [online]. 2016, vol.33, n.1, pp.300-308. ISSN 2215-5287.
The anomalies of pulmonary venous drainage due to alteration in early embryonic development of the pulmonary veins (right or left) while still connections are present with systemic veins (cardinal, umbilicovitelins). These malformations represent 0.4 to 2.0 % of all congenital heart diseases, with an incidence of 6.8 patients in every 100,000 births. Sixty eight percent of the cases are diagnosed in newborns, which indicates that most patients are symptomatic early in life. The infracardiac TAPVC represent 15 to 25% of all TAPVC.
Palavras-chave : Total anomalous pulmonary venous connection; pulmonary veins; supracardíac; infracardíac; cianosis; drain; “snow man image”.